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 The basal ganglia are connected structures within the cerebral

hemispheres and brainstem (Fig. 7.16). They include the caudate

nucleus and putamen (collectively known as the striatum), globus

pallidus, thalamus, subthalamic nucleus and substantia nigra

(the latter in the brainstem). The basal ganglia receive much

information from the cortex and are involved in regulating many

activities, principally control of movement, but are also involved

in eye movement, behaviour and executive function control.

Disorders of the basal ganglia may cause reduced movement

(typically Parkinsonism; p. 135) or, less commonly, excessive

movement such as ballism or tics (p. 137).

Assess the motor system using the following method:

assessment of stance and gait

inspection and palpation of muscles

assessment of tone

testing movement and power

examination of reflexes

testing coordination.

Stance and gait

Stance and gait depend on intact visual, vestibular, sensory,

corticospinal, extrapyramidal and cerebellar pathways, together

with functioning lower motor neurones and spinal reflexes.

Non-neurological gait disorders are discussed in on page 259.

Certain abnormal gait patterns are recognisable, suggesting

diagnoses (Box 7.7 and Fig. 7.17).

Examination sequence

Stance

• Ask the patient to stand with their (preferably bare) feet

close together and eyes open.

• Swaying, lurching or an inability to stand with the feet

together and eyes open suggests cerebellar ataxia.

• Ask the patient to close their eyes (Romberg’s test) but be

prepared to steady/catch them. Repeated falling is a

Fig. 7.15 Principal motor pathways.

7.6 Features of motor neurone lesions

Upper motor

neurone lesion

Lower motor

neurone lesion

Inspection Usually normal (may

be disuse wasting in

longstanding lesions)

Muscle wasting,

fasciculations

Tone Increased with

clonus

Normal or decreased,

no clonus

Weakness Preferentially affects

extensors in arms,

flexors in leg

Usually more focal,

in distribution of

nerve root or

peripheral nerve

Deep tendon reflexes Increased Decreased/absent

Plantar response Extensor (Babinski

sign)

Flexor

the nervous system, such as the basal ganglia and cerebellum,

have important modulating effects on movement. It is important

to distinguish upper from lower motor neurone signs to help

localise the lesion (Box 7.6).

Upper motor neurone lesions

If the lesion affects the CNS pathways, the lower motor neurones

are under the uninhibited influence of the spinal reflex. The motor

units then have an exaggerated response to stretch with increased

tone (spasticity), clonus and brisk reflexes. There is weakness but

not wasting (although atrophy may develop with longstanding

lesions). Primitive reflexes, such as the plantar extensor response

(Babinski sign), may be present.

Lower motor neurone lesions

Motor fibres, together with input from other systems involved in

the control of movement, including extrapyramidal, cerebellar,

vestibular and proprioceptive afferents, converge on the cell

bodies of lower motor neurones in the anterior horn of the grey

matter in the spinal cord (Fig. 7.15).

Motor system • 135

7

behind the patient, deliver a brisk push forwards or pull

backwards. You must be ready to catch them if they are

unable to maintain their balance. If in doubt, have an

assistant standing in front of the patient.

Gait

• Look at the patient’s shoes for abnormal wear patterns.

• Time the patient walking a measured 10 metres, with a

walking aid if needed, turning through 180 degrees and

returning.

• Note stride length, arm swing, steadiness (including

turning), limping or other difficulties.

• Look for abnormal movements that may be accentuated

by walking such as tremor (in Parkinson’s disease) or

dystonic movements.

• Listen for the slapping sound of a foot-drop gait.

• Ask the patient to walk first on their tiptoes, then heels.

Ankle dorsiflexion weakness (foot drop) is much more

common than plantar flexion weakness, and makes

walking on the heels difficult or impossible.

• Ask the patient to walk heel to toe in a straight line

(tandem gait). This emphasises gait ataxia and may be the

only abnormal finding in midline cerebellar (vermis) lesions.

Unsteadiness on standing with the eyes open is common in

cerebellar disorders. Instability that only occurs, or is markedly

worse, on eye closure (Romberg’s sign) indicates proprioceptive

sensory loss (sensory ataxia) or bilateral vestibular failure. Cerebellar

ataxia is not usually associated with a positive Romberg test.

Hemiplegic gait (unilateral upper motor neurone lesion) is

characterised by extension at the hip, knee and ankle and

circumduction at the hip, such that the foot on the affected

side is plantar flexed and describes a semicircle as the patient

walks. The upper limb may be flexed (Fig. 7.17A).

Bilateral upper motor neurone damage causes a scissor-like gait

due to spasticity. Cerebellar dysfunction leads to a broad-based,

unsteady (ataxic) gait, which usually makes walking heel to toe

impossible. In Parkinsonism, initiation of walking may be delayed;

the steps are short and shuffling with loss/reduction of arm

swing (Fig. 7.17D). A tremor may become more apparent. The

stooped posture and impairment of postural reflexes can result

in a festinant (rapid, short-stepped, hurrying) gait. As a doorway

or other obstacle approaches, the patient may freeze. Turning

involves many short steps, with the risk of falls. Postural instability

on the pull test, especially backwards, occurs in Parkinsonian

syndromes. Proximal muscle weakness may lead to a waddling

positive result. Swaying is common and should not be

misinterpreted.

• The ‘pull test’ assesses postural stability. Ask the patient

to stand with their feet slightly apart. Inform them that you

are going to push them forwards or pull them backwards.

They should maintain their position if possible. Standing

Globus pallidus

externa (GPe)

Globus pallidus

interna (GPi)

Thalamus

B

Subthalamic nucleus (STN)

Substantia nigra (SN)

Caudate

nucleus

Putamen

Striatum

Thalamus

Amygdala

Caudate

nucleus

Putamen

A

Fig. 7.16 Basal ganglia. A Anatomical location. B Coronal view.

7.7 Common gait abnormalities

Gait disturbance Description Causes

Parkinsonian Stooped posture

Shuffling (reduced

stride length)

Loss of arm swing

Postural instability

Freezing

Parkinson’s disease

and other Parkinsonian

syndromes

Gait apraxia Small, shuffling steps

(marche à petits pas)

Difficulty in starting to

walk/freezing

Better ‘cycling’ on bed

than walking

Cerebrovascular

disease

Hydrocephalus

Spastic Stiff ‘walking-throughmud’ or scissors gait

Spinal cord lesions

Myopathic Waddling (proximal

weakness)

Bilateral

Trendelenburg signs

Muscular dystrophies

and acquired

myopathies

Foot drop Foot slapping Neuropathies

Common peroneal

nerve palsy

L5 radiculopathy

Central ataxia Wide-based, ‘drunken’

Tandem gait poor

Cerebellar disease

Sensory ataxia Wide-based

Positive Romberg sign

Neuropathies

Spinal cord disorders

Functional Variable, often bizarre,

inconsistent

Knees flexed, buckling

Dragging immobile leg

behind

Functional neurological

disorders

© Crown Copyright.

136 • The nervous system

such as professional sports players, may have physiological

muscle hypertrophy. Pseudohypertrophy may occur in muscular

dystrophy but the muscles are weak.

Fasciculation

Fasciculations are visible irregular twitches of resting muscles

caused by individual motor units firing spontaneously. This occurs

in lower motor neurone disease, usually in wasted muscles.

Fasciculation is seen, not felt, and you may need to observe

carefully for several minutes to be sure that it is not present.

Physiological (benign) fasciculation is common, especially in the

calves, but is not associated with weakness or wasting. Myokymia

– fine, involuntary fascicular contractions – involves rapid bursts

of repetitive motor unit activity that often affects orbicularis oculi

or the first dorsal interosseus, and is rarely pathological.

Abnormal movements

Myoclonic jerks

These are sudden, shock-like contractions of one or more muscles

that may be focal or diffuse and occur singly or repetitively.

Healthy people commonly experience these when falling asleep

(hypnic jerks). They may also occur pathologically in association

with epilepsy, diffuse brain damage and some neurodegenerative

disorders such as prion diseases. Negative myoclonus (asterixis)

is seen most commonly in liver disease (liver flap).

gait with bilateral Trendelenburg signs (see p. 259 and Fig. 13.37).

Bizarre gaits, such as when patients drag a leg behind them,

are often functional but some diseases, including Huntington’s

disease, produce unusual and chaotic gaits.

Inspection and palpation of the muscles

Examination sequence

• Completely expose the patient while maintaining their

comfort and dignity.

• Look for asymmetry, inspecting both proximally and

distally. Note deformities, such as flexion deformities or

pes cavus (high foot arches).

Inspect for wasting or hypertrophy, fasciculation and

involuntary movement.

Muscle bulk

Lower motor neurone lesions may cause muscle wasting. This

is not seen in acute upper motor neurone lesions, although

disuse atrophy may develop with longstanding lesions. A motor

neurone lesion in childhood may impair growth (causing a smaller

limb or hemiatrophy) or lead to limb deformity, such as pes

cavus. Muscle disorders usually result in proximal wasting (the

notable exception is myotonic dystrophy, in which it is distal,

often with temporalis wasting). People in certain occupations,

A Spastic hemiparesis

One arm held immobile and

 close to the side with elbow,

wrist and fingers flexed

Leg extended with plantar

flexion of the foot

On walking, the foot is

dragged, scraping the toe

in a circle (circumduction)

Caused by upper motor

neurone lesion, e.g. stroke

B Steppage gait

 Foot is dragged or lifted high

 and slapped on to the floor

 Unable to walk on the heels

 Caused by foot drop owing to

 lower motor neurone lesion

C Sensory or cerebellar ataxia

 Gait is unsteady and wide-

 based. Feet are thrown forward

 and outward and brought down

 on the heels

In sensory ataxia, patients watch

 the ground. With their eyes

 closed, they cannot stand

 steadily (positive Romberg sign)

 In cerebellar ataxia, turns are

 difficult and patients cannot

 stand steadily with feet together

 whether eyes are open or

 closed

 Caused by polyneuropathy or

 posterior column damage, e.g.

 syphilis

D Parkinsonian gait

 Posture is stooped with head

 and neck forwards

 Arms are flexed at elbows and

 wrists. Little arm swing

 Steps are short and shuffling

 and patient is slow in getting

 started (festinant gait)

 Caused by lesions in the basal

 ganglia

Fig. 7.17 Abnormalities of gait.

Motor system • 137

7

• Passively move each joint to be tested through as full

a range as possible, both slowly and quickly in all

anatomically possible directions. Be unpredictable with

these movements, in both direction and speed, to prevent

the patient actively moving with you; you want to assess

passive tone. It may be helpful to distract the patient

by asking them to count backwards from 20 while

assessing tone.

Upper limb

• Hold the patient’s hand as if shaking hands, using your

other hand to support their elbow. Assess tone at the

wrist and elbow with supination/pronation and flexion/

extension movements.

• Activation (or synkinesis) is a technique used to

exaggerate subtle increase in tone, and is particularly

useful for assessing extrapyramidal tone increase. Ask the

patient to describe circles in the air with the contralateral

limb while you assess tone. A transient increase in tone

with this manœuvre (Froment’s) is normal.

Lower limb

• Roll the leg from side to side and then briskly flip the knee

up into a flexed position, observing the movement of the

foot. Typically, the heel moves up the bed, but increased

tone may cause it to lift off the bed due to failure of

relaxation.

Ankle clonus

• Support the patient’s leg, with both the knee and the

ankle resting in 90-degree flexion.

• Briskly dorsiflex and partially evert the foot, sustaining the

pressure. Clonus is felt as repeated beats of dorsiflexion/

plantar flexion.

Myotonia

• Ask the patient to make a fist and then to relax and open

their hand; watch for the speed of relaxation.

• Using the tendon hammer, percuss the belly of the thenar

eminence; this may induce contraction of the muscles,

causing the thumb to adduct, and you may witness

dimpling of the muscle belly.

Hypotonia

Decreased tone may occur in lower motor neurone lesions

and is usually associated with muscle wasting, weakness and

hyporeflexia. It may also be a feature of cerebellar disease or

signal the early phases of cerebral or spinal shock, when the

paralysed limbs are atonic prior to developing spasticity. Reduced

tone can be difficult to elicit.

Hypertonia

Increased tone may occur in two main forms: spasticity and

rigidity.

Spasticity is velocity-dependent resistance to passive

movement: it is detected with quick movements and is a feature

of upper motor neurone lesions. It is usually accompanied by

weakness, hyper-reflexia, an extensor plantar response and

sometimes clonus. In mild forms it is detected as a ‘catch’ at

the beginning or end of passive movement. In severe cases

it limits the range of movement and may be associated with

contractures. In the upper limbs it may be more obvious

on attempted extension; in the legs it is more evident on

flexion.

Tremor

Tremor is an involuntary, oscillatory movement about a joint

or a group of joints, resulting from alternating contraction and

relaxation of muscles. Tremors are classified according to their

frequency, amplitude, position (at rest, on posture or movement)

and body part affected.

Physiological tremor is a fine (low-amplitude), fast (highfrequency, 3–30 Hz) postural tremor. A similar tremor occurs in

hyperthyroidism and with excess alcohol or caffeine intake, and

is a common adverse effect of beta-agonist bronchodilators.

Essential tremor is the most common pathological cause of

tremor; it is typically symmetrical in the upper limbs and may

involve the head and voice. The tremor is noted on posture and

with movement (kinetic). It may be improved by alcohol and often

demonstrates an autosomal dominant pattern of inheritance.

Parkinson’s disease causes a slow (3–7 Hz), coarse, ‘pill-rolling’

tremor, worse at rest but reduced with voluntary movement. It is

more common in the upper limbs, is usually asymmetrical and

does not affect the head, although it may involve the jaw/chin

and sometimes the legs.

Isolated head tremor is usually dystonic and may be associated

with abnormal neck postures such as torticollis, antecollis or

retrocollis.

Intention tremor is absent at rest but maximal on movement

and on approaching the target (hunting tremor), and is usually

due to cerebellar damage. It is assessed with the finger-to-nose

test (p. 141).

Other causes of tremor include hereditary or acquired

demyelinating neuropathies (such as Charcot–Marie–Tooth

disease) and are termed neuropathic tremors. Drugs commonly

causing tremor include sodium valproate, glucocorticoids and

lithium.

Movement disorders, including tremor, are common functional

symptoms. They are often inconsistent and distractible, with

varying frequencies and amplitudes, and may be associated

with other functional signs.

Other involuntary movements

These are classified according to their appearance.

Dystonia is caused by sustained muscle contractions, leading to

twisting, repetitive movements and sometimes tremor. It may be

focal (as in torticollis), segmental (affecting two or more adjacent

body parts) or generalised.

Chorea describes brief, jerky, random, purposeless movements

that may affect various body parts, commonly the arms.

Athetosis is a slower, writhing movement, more similar to

dystonia than chorea.

Ballism refers to violent flinging movements sometimes affecting

only one side of the body (hemiballismus).

Tics are repetitive, stereotyped movements that may be briefly

suppressed by the patient.

Tone

Tone is the resistance felt by the examiner when moving a joint

passively.

Examination sequence

• Ask the patient to lie supine on the examination couch

and to relax and ‘go floppy’. Enquire about any pain or

limitations of movement before proceeding.

138 • The nervous system

Examination sequence

Do not test every muscle in most patients; the commonly

tested muscles are listed in Box 7.9.

• Ask about pain that might interfere with testing.

• Observe the patient getting up from a chair and walking.

• Test upper limb power with the patient sitting on the edge

of the couch. Test lower limb power with the patient

reclining.

• Ask the patient to lift their arms above their head.

• Ask them to ‘play the piano’. Check movements of the

fingers; asymmetric loss of fine finger movement may be a

very early sign of cortical or extrapyramidal disease.

• Observe the patient with their arms outstretched and

supinated (palms up) and their eyes closed for ‘pronator

drift’, when one arm starts to pronate.

7.8 Medical Research Council grading of muscle power

Grade Description

0 No muscle contraction visible

1 Flicker of contraction but no movement

2 Joint movement when effect of gravity eliminated

3 Movement against gravity but not against resistance

4a Movement against resistance but weaker than normal

5 Normal power

a

May be further classified as 4+ or 4−.

7.9 Nerve and muscle supplies of commonly tested movements

Movement Muscle Nerve and root

Shoulder abduction Deltoid Axillary C5

Elbow flexion Bicepsa Musculocutaneous C5a

/6

Brachioradialis (supinator reflex)a Radial C6a

Elbow extension Tricepsa Radial C7

Wrist extension Extensor carpi radialis longus Posterior interosseous C6

Finger extension Extensor digitorum communis Posterior interosseous C7

Finger flexion Flexor pollicis longus (thumb)

Flexor digitorum profundus (index and middle fingers)

Anterior interosseous C8

Flexor digitorum profundus (ring and little fingers) Ulnar C8

Finger abduction First dorsal interosseous Ulnar T1

Thumb abduction Abductor pollicis brevis Median T1

Hip flexion Iliopsoas Iliofemoral nerve L1/2

Hip extension Gluteus maximus Sciatic L5/S1

Knee flexion Hamstrings Sciatic S1

Knee extension Quadricepsa Femoral L3a

/4

Ankle dorsiflexion Tibialis anterior Deep peroneal L4/5

Ankle plantar flexion Gastrocnemius and soleusa Tibial S1a

/2

Great toe extension (dorsiflexion) Extensor hallucis longus Deep peroneal L5

Ankle eversion Peronei Superficial peroneal L5/S1

Ankle inversion Tibialis posterior Tibial nerve L4/5

a

Indicates nerve root innervation of commonly elicited deep tendon reflexes.

Rigidity is a sustained resistance throughout the range of

movement and is most easily detected when the limb is moved

slowly. In Parkinsonism this is classically described as ‘lead

pipe’ rigidity. In the presence of a Parkinsonian tremor there

may be a regular interruption to the movement, giving it a jerky

feel (‘cog wheeling’).

Clonus

Clonus is a rhythmic series of contractions evoked by a sudden

stretch of the muscle and tendon. Unsustained (<6 beats) clonus

may be physiological. When sustained, it indicates upper motor

neurone damage and is accompanied by spasticity. It is best

elicited at the ankle; knee (patella) clonus is rare and not routinely

tested.

Myotonia

Myotonia refers to the inability of muscles to relax normally and

characterises a group of neuromuscular disorders, the most

common of which is myotonic dystrophy. Patients may notice

difficulty in letting go of things with their hands, or a stiff gait.

Power

Strength varies with age, occupation and fitness. Grade muscle

power using the Medical Research Council (MRC) scale (Box

7.8). Record what patients can do in terms of daily activities;

for example, whether they can stand, walk and raise both arms

above their head. Lesions at different sites produce different

clinical patterns of weakness; examination will help discriminate

upper from lower motor neurone lesions.

Motor system • 139

7

weakness. This is helpful both diagnostically and therapeutically,

as you can show patients that their leg is not actually weak

using this sign.

Deep tendon reflexes

Anatomy

A tendon reflex is the involuntary contraction of a muscle in

response to stretch. It is mediated by a reflex arc consisting

of an afferent (sensory) and an efferent (motor) neurone with

one synapse between (a monosynaptic reflex). Muscle stretch

activates the muscle spindles, which send a burst of afferent

signals that lead to direct efferent impulses, causing muscle

contraction. These stretch reflex arcs are served by a particular

spinal cord segment that is modified by descending upper motor

neurones. The most important reflexes are the deep tendon

and plantar responses, whereas others, such as abdominal and

cremasteric reflexes, are rarely tested and of questionable value.

Dermatomal involvement may further help localise a lesion; for

example, pain going down one leg, with an absent ankle jerk

(S1) and sensory loss on the sole of the foot (S1 dermatome),

localises to the S1 root, most commonly due to a prolapsed

intervertebral disc (sciatica).

Examination sequence

• Ask the patient to lie supine on the examination couch

with the limbs exposed. They should be as relaxed and

comfortable as possible, as anxiety and pain can cause an

increased response.

• Extend your wrist and allow the weight of the tendon

hammer head to determine the strength of the blow. Strike

your finger that is palpating the biceps and supinator

tendons (otherwise it is painful for the patient), or the

tendon itself for the triceps, knee and ankle jerks.

• Record the response as:

• increased (+++)

• normal (++)

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